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JOURNAL OF MEDICAL AND SURGICAL RESEARCH - edvsdf, efrb

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Idiopathic Sclerosing Encapsulating Peritonitis (Abdominal Cocoon Syndrome)

Author: Abdelaziz Amine, Mohammed Idrissi

Category: JMSR Surgery

Abstract:

Primary sclerosing encapsulating peritonitis, also known as abdominal cocoon syndrome is an unusual cause of bowel obstruction. If sclerosing encapsulating peritonitis may be secondary to peritoneal dialysis, tuberculosis, intraperitoneal chemotherapy or drug consumption, the idiopathic forms are exceptional. The physiopathology is an encasement of intestines by a fibrocollagenous membrane. This is a case of 53 year-old women with primary sclerosing encapsulating peritonitis admitted for bowel occlusion. Abdominal CT scan was performed (Figures A & B) and diagnosis was confirmed per-operatively (Figures C & D). The patient was discharged in day3. Etiological investigations were negative concluding to an idipathic form of sclerosing encapsulating peritonitis.

Keywords: Cocoon syndrome, Idiopathic, Occlusion, Sclerosing peritonitis, Surgery

Full Text:

Primary sclerosing encapsulating peritonitis, also known as abdominal cocoon syndrome is an unusual cause of bowel obstruction. If sclerosing encapsulating peritonitis may be secondary to peritoneal dialysis, tuberculosis, intraperitoneal chemotherapy or drug consumption, the idiopathic forms are exceptional. The physiopathology is an encasement of intestines by a fibrocollagenous membrane. This is a case of 53 year-old women with primary sclerosing encapsulating peritonitis admitted for bowel occlusion. Abdominal CT scan was performed (Figures A & B) and diagnosis was confirmed per-operatively (Figures C & D) [Video]. The patient was discharged in day3. Etiological investigations were negative concluding to an idipathic form of sclerosing encapsulating peritonitis.

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